PKU kudya kunodiwa kuvanhu vane genetic disorder inonzi phenylketonuria (PKU). Vanhu vane phenylketonuria haasisina enzyme inobvumira muviri kuti uchinje phenylalanine (an amino acid) kune tyrosine (imwe amino acid ). I phenylalanine inovaka uye inoita kuti uropi hukuvara; saka munhu wose ane PKU anofanira kudzivisa kudya kweprotein-rich.
Vana vacheche nemucheche vane PKU vanoda mushonga chaiwo usina phenylalanine.
Zvinonyanya kukosha kuti vana, vaduku, uye vana havadyi mapuroteni-richine zvibereko nokuti uropi huri kukura nokukurumidza. Kudya kwakasimba kunofanira kuteverwa. Zvokudya zvose izvo zvakakwirira mumapuroteni zvinoda kudziviswa.
Zvokudya zvakakwirira mumapuroteni zvinosanganisira:
- nyama
- hove
- huku
- mukaka
- yogurt
- cheese
- mazai
- nuts
- Mbeu
- legumes
- peanut uye imwe nut butter
Zvokudya, zvokudya zvinonaka, uye zvokudya zvinogadzirwa nezvinhu izvi zvinoda kudzivirirwa zvakare - saka pizza, keke, makiki, hamburgers, imbwa dzinopisa, ice cream, yogurt nezvimwe zvizhinji zvekudya. Kunyange zvinhu zvakadai sechingwa nemamwe marudzi ezviyo zvinogona kuva nemaprotheni akawanda. Aspartame zvakare inofanira kudziviswa sezvo iri kusanganiswa kweaspartic acid uye phenylalanine.
Vana nevechiri kuyaruka vane PKU vanogona kudya michero nemiriwo uye zvishoma zvezviyo uye zvipuka nokuti izvo zvokudya zvinoderera mumapuroteni. Vanhu vakuru vanoda kubatisisa zvakanyatsonaka kune zvekudya pamwe chete.
Asi, chirongwa chePKU chakanyanya kuderera muprotheni yehutano hwakanaka, saka vana nevakuru vane PKU vanoda kudya mapuroteni anokonzerwa zvakagadzirwa pasina phenylalanine.
Uyewo, chikafu ichi chinoda kuteverwa kwehupenyu, uye kuongororwa kweropa kunowanzoitwa kuitira kuchengetedza nhengo dze phenylalanine mumuviri.
Is PKU Common?
Maererano neNational PKU Alliance, inenge imwe muvana 15 000 vane PKU. Vacheche muUnited States uye dzimwe nyika dzakawanda dzakaongororwa nguva pfupi mushure mekuberekwa, uye chero bedzi vana vacheche nevana vanonamatira kune kudya, ubongo hwavo huchakura zvakanaka.
Vakuru nevane PKU vangave vaine zvishoma zvishoma neprotein yekunwa nokuti uropi hwakagadzirwa zvakakwana, asi PKU haifaniri kuenda uye kudya zvakanyanya phenylalanine inogona kukonzera zvinetso zvepfungwa uye kurasikirwa mupfungwa.
Sources:
Maher AK. "Zviri nyore Diet Menu." Gwaro Regumi nerimwe, Hoboken NJ, USA: Wiley-Blackwell Publishing, Gunyana 2011.
Merck Manual - Professional Version. "Amino Acid uye Organic Acid Metabolism Disorders." http://www.merckmanuals.com/professional/pediatrics/inherited-disorders-of-metabolism/overview-of-amino-acid-and-organic-acid-metabolism-disorders.
National Phenylketonuria Alliance. "Phenylketonuria Facts for Faculty School and Staff." http://www.npkua.org/Portals/0/PKU_schoolfacts.pdf .